{"created":"2023-06-19T10:30:05.831466+00:00","id":2186,"links":{},"metadata":{"_buckets":{"deposit":"1216ab00-6c95-43fb-98e6-5e82a913de78"},"_deposit":{"created_by":3,"id":"2186","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"2186"},"status":"published"},"_oai":{"id":"oai:kwmed.repo.nii.ac.jp:00002186","sets":["1709617079800:37:687"]},"author_link":["125015","125025","125023","125020","125014","125024","125017","125022","125018","125016","125013","125021","125019"],"item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2019","bibliographicIssueDateType":"Issued"},"bibliographicPageEnd":"14","bibliographicPageStart":"9","bibliographicVolumeNumber":"45","bibliographic_titles":[{},{"bibliographic_title":"Kawasaki medical journal","bibliographic_titleLang":"en"}]}]},"item_10001_description_34":{"attribute_name":"記事種別(英)","attribute_value_mlt":[{"subitem_description":"Case Report","subitem_description_type":"Other"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"Kawasaki Medical Society"}]},"item_10001_relation_14":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.11482/KMJ-E201945009","subitem_relation_type_select":"DOI"}}]},"item_10001_relation_17":{"attribute_name":"関連サイト","attribute_value_mlt":[{"subitem_relation_name":[{}],"subitem_relation_type_id":{"subitem_relation_type_id_text":"http://igakkai.kms-igakkai.com/wp/wp-content/uploads/2019en/KMJ-E201945009.pdf","subitem_relation_type_select":"URI"}}]},"item_10001_relation_35":{"attribute_name":"医中誌ID","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"2020354373","subitem_relation_type_select":"ICHUSHI"}}]},"item_10001_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AA12685295","subitem_source_identifier_type":"NCID"},{"subitem_source_identifier":"AA12029005","subitem_source_identifier_type":"NCID"}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"03850234","subitem_source_identifier_type":"ISSN"},{"subitem_source_identifier":"24343404","subitem_source_identifier_type":"ISSN"}]},"item_10001_text_32":{"attribute_name":"著者所属(英)","attribute_value_mlt":[{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of Pediatrics, Kawasaki Medical School"}]},"item_10001_textarea_5":{"attribute_name":"抄録(英)","attribute_value_mlt":[{"subitem_textarea_language":"en","subitem_textarea_value":" RAS -associated autoimmune leukoproliferative disorder (RALD) is a recently reported rare nonmalignant autoimmune disorder. The characteristic clinical findings of RALD include monocytosis, leukocytosis, lymphoproliferation, and autoimmune phenomena. RALD is defined by somatic mutations in KRAS or NRAS . It is a new disease that was reported by Niemela and Takagi in 2011. The prognosis and incidence are currently unknown and the treatment strategy has not yet been established.\n Here we describe the long-term survival of a patient with who displayed a somatic KRAS G12D mutation. His clinical features and labolatory data were overlapped with juvenile myelomonocytic leukemia and chronic myelomonocytic leukemia. Mercaptopurine hydrate, hydroxycarbamide and azacitizine were administered to control white blood cell count and improve clinical symptoms. He had a long survival time without hematopoietic stem cell transplantation."}]},"item_10001_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"TERANISHI, Hideto","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"WAKABAYASHI, Shoko","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KONO, Mina","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"ONO, Sahoko","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KATO, Atsushi","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KONDO, Eisuke","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"AKAIKE, Hiroto","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"MIYATA, Ippei","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OGITA, Satoko","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OHNO, Naoki","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OISHI, Tomohiro","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"MASUNO, Mitsuo","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OUCHI, Kazunobu","creatorNameLang":"en"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2020-04-01"}],"displaytype":"detail","filename":"KMJ-E201945009.pdf","filesize":[{"value":"841.3 kB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"PDF","url":"https://kwmed.repo.nii.ac.jp/record/2186/files/KMJ-E201945009.pdf"},"version_id":"2e479820-00e6-4427-bd3c-985dc782cbcc"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"RAS-associated autoimmune leukoproliferative disorder","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"azacitizine","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Long-term survival with RAS-associated autoimmune leukoproliferative disorder with somatic KRAS mutation:A case report","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Long-term survival with RAS-associated autoimmune leukoproliferative disorder with somatic KRAS mutation:A case report","subitem_title_language":"en"}]},"item_type_id":"10001","owner":"3","path":["687"],"pubdate":{"attribute_name":"公開日","attribute_value":"2020-04-01"},"publish_date":"2020-04-01","publish_status":"0","recid":"2186","relation_version_is_last":true,"title":["Long-term survival with RAS-associated autoimmune leukoproliferative disorder with somatic KRAS mutation:A case report"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-06-19T11:08:45.671923+00:00"}