{"created":"2023-06-19T10:30:47.582172+00:00","id":2933,"links":{},"metadata":{"_buckets":{"deposit":"da53bbe4-b943-4310-b083-7998aa8cb3d6"},"_deposit":{"created_by":3,"id":"2933","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"2933"},"status":"published"},"_oai":{"id":"oai:kwmed.repo.nii.ac.jp:00002933","sets":["1709617079800:37:792"]},"author_link":["124965","124967","124966","124964","124968","124969","124963"],"item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2020","bibliographicIssueDateType":"Issued"},"bibliographicPageEnd":"151","bibliographicPageStart":"145","bibliographicVolumeNumber":"46","bibliographic_titles":[{},{"bibliographic_title":"Kawasaki medical journal","bibliographic_titleLang":"en"}]}]},"item_10001_description_34":{"attribute_name":"記事種別(英)","attribute_value_mlt":[{"subitem_description":"Case Report","subitem_description_type":"Other"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"Kawasaki Medical Society"}]},"item_10001_relation_14":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.11482/KMJ-E202046145","subitem_relation_type_select":"DOI"}}]},"item_10001_relation_17":{"attribute_name":"関連サイト","attribute_value_mlt":[{"subitem_relation_name":[{}],"subitem_relation_type_id":{"subitem_relation_type_id_text":"https://igakkai.kms-igakkai.com/wp/wp-content/uploads/2020en/KMJ-E202046145.pdf","subitem_relation_type_select":"URI"}}]},"item_10001_relation_35":{"attribute_name":"医中誌ID","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"2022017995","subitem_relation_type_select":"ICHUSHI"}}]},"item_10001_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AA12685295","subitem_source_identifier_type":"NCID"},{"subitem_source_identifier":"AA12029005","subitem_source_identifier_type":"NCID"}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"03850234","subitem_source_identifier_type":"ISSN"},{"subitem_source_identifier":"24343404","subitem_source_identifier_type":"ISSN"}]},"item_10001_text_32":{"attribute_name":"著者所属(英)","attribute_value_mlt":[{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"},{"subitem_text_language":"en","subitem_text_value":"Department of General Surgery, Kawasaki Medical School"}]},"item_10001_textarea_5":{"attribute_name":"抄録(英)","attribute_value_mlt":[{"subitem_textarea_language":"en","subitem_textarea_value":"　Fabry disease is a rare genetic disease, and surgical reports for the patients with Fabry disease are also rarer.\n　A 58-year-old man presented with chest pain. At the age of 40, he commenced dialysis due to chronic renal failure and at the age of 50, he developed shortness of breath on exertion, and echocardiography showed mitral regurgitation and left ventricular hypertrophy. He was then diagnosed with Fabry disease due to decreased alpha-galactosidase activity. This diagnosis led to enzyme replacement therapy (ERT). The ERT was effective as he had not never experienced further exacerbation of congestive heart failure. While the CHF was put under control, his mitral stenosis gradually worsened, and the patient began to have more chest pain and became hypotensive. He then referred to our section for mitral valve replacement. His mitral annulus was severely calcified and we removed mitral annulus calcification (MAC) at minimum so that we could stich needles and implanted mechanical valve. Paroxysmal atrial fibrillation and bradycardia made his hemodynamics unstable against ERT, which also caused low dialysis efficiency. It took longer than usual to wean him off catecholamines. His hemodynamics became more stable and dialysis efficiency generally improved, so he moved from ICU to ward on postoperative day 11. On day 32, he was transferred back to the referring hospital for his rehabilitation.\n　We have reported a surgical case of Fabry disease, that are not only rare but have high perioperative risk due to Fabry disease’s specific complications."}]},"item_10001_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"WATANABE, Tatsuya","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"TOKUNAGA, Noriyuki","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"TSUJIMOTO, Kotone","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KONDO, Kensuke","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"YOSHIDA, Hideo","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KUINOSE, Masahiko","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"YAMATSUJI, Tomoki","creatorNameLang":"en"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2022-10-21"}],"displaytype":"detail","filename":"KMJ-E202046145.pdf","filesize":[{"value":"3.3 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"PDF","url":"https://kwmed.repo.nii.ac.jp/record/2933/files/KMJ-E202046145.pdf"},"version_id":"72019a97-f381-419e-a9ac-49e4b35d3b05"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Mitral stenosis","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Fabry disease","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Mitral valve replacement","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Enzyme replacement therapy","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"A surgical case of mitral valve replacement for a patient with Fabry disease complicated with hemodialysis","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"A surgical case of mitral valve replacement for a patient with Fabry disease complicated with hemodialysis","subitem_title_language":"en"}]},"item_type_id":"10001","owner":"3","path":["792"],"pubdate":{"attribute_name":"公開日","attribute_value":"2022-10-21"},"publish_date":"2022-10-21","publish_status":"0","recid":"2933","relation_version_is_last":true,"title":["A surgical case of mitral valve replacement for a patient with Fabry disease complicated with hemodialysis"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-06-19T11:08:56.177080+00:00"}